The different structure of the skin in the Ehlers-Danlos syndromes makes it more fragile than normal skin. Stretchiness, abnormal scarring, stretch marks at a young age, easy bruising and slow wound healing are all signs of EDS, but the presence and severity of these issues will depend on the type.
Keeping this in consideration, does Ehlers Danlos get worse with age?
Many of the problems associated with EDS are progressive, meaning that they get worse over time.
Thereof, does hypermobility affect the skin?
joint hypermobility. loose, unstable joints that dislocate easily. stretchy skin. fragile skin that can split easily, especially over the forehead, knees, shins and elbows.
Does Ehlers Danlos make you look older?
Due to the collagen in the skin being extra stretchy, many EDS patients experience a lack of wrinkles as they age. This collagen may help EDS patients look younger and can also cause skin to feel extremely soft. Doctor’s even describe the skin as “velvet-soft”.
What does EDS pain feel like?
I was asked recently to describe what my body feels with EDS. I described the feeling of being tenderized with a mallet all over my body. Not enough to break bones, but hard enough to leave bruises. This is my daily experience even with the aid of pain meds.
Does EDS affect teeth?
While many people with EDS not have any notable oral problems specifically due to EDS, this connective tissue disorder can affect the teeth and gums as well as the temporomandibular joint. In addition, the systemic complications of EDS could sometimes compromise the delivery of routine dental care.
What is the lifespan of someone with EDS?
People affected by vascular EDS have a median life expectancy of 48 years and many will have a major event by age 40.
Is Ehlers-Danlos considered a disability?
If you have vascular or regular EDS with severe symptoms that prevent you from working, you may be able to get disability. … Ehlers–Danlos can affect your skin, joints, and blood vessel walls; the syndrome is characterized by extremely flexible joints and very stretchy, fragile skin.
Why are EDS patients called zebras?
According to the international Ehlers-Danlos Society, the reference to zebras is borrowed from a common expression heard in medicine: “When you hear hoofbeats behind you, don’t expect to see a zebra.” In other words, medical professionals are typically taught to look out for more-common ailments rather than testing for …
At what age is Ehlers Danlos Syndrome diagnosed?
The mean age of patients was 41 years (the mean age at diagnosis: 28 years). Overall, each patient with EDS required an average of 12 different kinds of medical services in relation to their disease (three more than the average number of services required by the 16 rare diseases surveyed).
What happens to collagen in Ehlers Danlos?
Classical Ehlers–Danlos syndrome (EDS) is characterized by skin hyperelasticity, joint hypermobility, increased tendency to bruise, and abnormal scarring. Mutations in type V collagen, a regulator of type I collagen fibrillogenesis, have been shown to underlie this type of EDS.
What is the difference between Ehlers Danlos and joint hypermobility syndrome?
While hypermobile EDS (hEDS) remains the only EDS without a confirmed cause, the criteria for hEDS diagnosis have been tightened compared to the 1997 Villefranche nosology as determined by international consensus. The essential difference between HSD and hEDS lies in the stricter criteria for hEDS compared to the HSD.
Can you have Eds without stretchy skin?
Skin and Connective Tissue: People with hEDS do NOT have to have profoundly stretchy skin! Most notably, in hEDS, the degree of softness, stretchiness, fragility, bruisability, and poor wound healing of skin differs from “normal” subjects but is mild in comparison to other types of EDS.
How rare is hypermobility EDS?
Video: Hypermobility EDS – an update
Vascular Ehlers Danlos syndrome (vEDS) is a rare disorder, estimated to affect between 1 in 50,000 and 1 in 200,000 people. It is caused by a gene mutation affecting a major protein, which causes weakness in vessel walls and hollow organs.